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Table 3 Cardiac anomalies associated with omphalocele. Stratified by syndromic or non-syndromic

From: Omphalocele: clinical and epidemiological profile of patients born in a tertiary care center in Rio de Janeiro

 

Non-syndromic

Syndromic

Unspecified aneuploidy

Malformation sequence

n (%) *

TOF

3

1

0

0

4 (23.5)

Coarctation of Aorta

0

1

0

0

1 (5.9)

ASD

1

1

0

0

2 (11.8)

VSD

2

0

1

0

3 (17.6)

VSD + ASD

0

1

0

0

1 (5.9)

VSD + PLSVC

0

1

0

0

1 (5.9)

Complex Heart Disease

1

0

0

0

1 (5.9)

Total AVSD

0

1

0

0

1 (5.9)

Acardia

1

0

0

0

1 (5.9)

HLHS

1

0

0

0

1 (5.9)

  1. *Related to the total number of patients with omphalocele (37).
  2. TOF – tetralogy of Fallot, ASD - atrial septal defect, VSD – ventricular septal defect, AVSD – atrioventricular septal defect, PLSVC - Persistent left superior vena cava, HLHS – hypoplastic left heart syndrome.